日本小児循環器学会雑誌 Pediatric Cardiology and Cardiac Surgery

Patients with total anomalous pulmonary venous connection accompanying pulmonary venous obstruction require early interventions soon after birth. We experienced the case of a preterm baby with infracardiac total anomalous pulmonary venous connection and an obstructive vertical vein who underwent preemptive stent implantation and repetitive stent dilatation followed by elective corrective surgery. The patient was delivered at 32 weeks and 5 days of gestation and birth weight 1,284 g. Systemic oxygen saturation was 86％, and a chest X-ray showed pulmonary congestion. At the age of 4 days, a stent was placed at the obstructive ductus venosus, which required transcatheter stent dilatation due to in-stent stenosis at the age of 29 and 38 days. At last, intracardiac repair was performed with weight of 1,849 g at the age of 57 days. Stent implantation for an obstructive vertical vein is feasible and effective even in preterm or low birth weight infants with total anomalous pulmonary venous connection and an obstructive vertical vein.