日本小児循環器学会雑誌 Pediatric Cardiology and Cardiac Surgery

Congenital right atrial appendage aneurysm is a rare heart disease, with only a few dozen cases worldwide since the report by Morrow et al. in 1968. Complications include arrhythmia, thromboembolism, palpitation, and dyspnea. Appropriate diagnosis and treatment are important, but guidelines are not yet established. The patient’s mother was referred to our hospital at 29 weeks of gestation for enlarged right atrium. Fetal echocardiography revealed a 14.2×7.9 mm (0.7 cm²) aneurysm, which was diagnosed as congenital right atrial aneurysm. Based on the aneurysm size at diagnosis (＜20×13 mm, ＜2 cm²), it was decided that the patient could be followed-up without treatment, and the baby was born without complications. At birth, the aneurysm size was 22×11 mm (1.7 cm²), and the ratio of the aneurysm size to the right atrium was unchanged from the fetal period. The patient is now nearing 1 year old without any complications. We think that the aneurysm size can guide the follow-up of congenital right atrial appendage aneurysms.