日本小児循環器学会雑誌 Pediatric Cardiology and Cardiac Surgery

Providing safe management to enable women with inherited primary arrhythmia syndromes (IPAS) to have babies is very important, but no management policy has yet been established. To obtain clinical information about pregnancy in women with IPAS and provide an input on the development of a management policy, we retrospectively reviewed the clinical records of six pregnancies in three patients with catecholaminergic polymorphic ventricular tachycardia (one suspected case) and one pregnancy in one patient with long QT syndrome in our hospital from 2008 to 2016. We held multidisciplinary meetings with obstetricians, cardiologists, anesthesiologists, and neonatologists to develop a detailed plan. With the exception of one patient, we selected a planned cesarean section between 37 and 38 weeks of gestation; there were no cardiac events. In the pursuit of a secure management strategy, the accumulating of additional clinical information and cases of pregnancy in women with IPAS is needed.