日本小児循環器学会雑誌 Pediatric Cardiology and Cardiac Surgery

We report a very unusual case of a double-chambered left ventricle. A muscular partition, in the left ventricle, associated with a double-chambered left ventricle, was discovered in a boy aged 14 months. No cardiac structural abnormality had been detected previously. At the age of two years, and weight of 11 kg, he was admitted to our medical center because of a systemic convulsion. Further diagnosis was made, considering brain infarction because of a left ventricular thrombus. Preoperative echocardiography showed severely depressed function of the apical chamber of the left ventricle with an embedded thrombus. The patient required an urgent thrombectomy concomitant with partial resection of the muscular partition wall between the apical and outlet chambers. Complete resection of the partition would have led to mitral valve dysfunction because of its continuity with the mitral papillary muscle. Postoperatively, the patient has been doing well with neither thrombus formation nor cardiac dysfunction.