日本小児循環器学会雑誌 Pediatric Cardiology and Cardiac Surgery

The surgical outcome of the Fontan operation has improved with refinements of the surgical technique and advances in perioperative management. As a large number of patients survive to adult after the surgery, the factors responsible for deterioration of patient quality of life have become important concerns. To maintain a sufficient Fontan circulation, catheterization or surgical re-intervention must be considered at the appropriate time together with meticulous follow-up and medical treatment.