日本小児循環器学会雑誌 Pediatric Cardiology and Cardiac Surgery

Cardiac inflammatory myofibroblastic tumors are very rare, and the clinical features are not well understood. We present the case of a 3-month-old girl with a confirmed pathological diagnosis of cardiac inflammatory myofibroblastic tumor. She was initially brought to hospital due to vomiting. She exhibited elevated serum IL-6 levels and other clinical symptoms suggestive of myxoma. Echocardiogram confirmed the presence of a large tumor of the right atrium and abundant pericardial effusion. We were concerned about the possibility of cardiac tamponade and considered the case to be urgent; we therefore recommended surgical removal of the tumor. This patient is also at risk for malignant transformation or recurrence of the cardiac inflammatory myofibroblastic tumor and needs a long-term follow-up.