Online ISSN: 2187-2988 Print ISSN: 0911-1794
特定非営利活動法人日本小児循環器学会 Japanese Society of Pediatric Cardiology and Cardiac Surgery
Pediatric Cardiology and Cardiac Surgery 35(4): 271-276 (2019)


先天性心疾患を有する18トリソミー児に対する姑息術が在宅移行へ与える効果Effects of Palliative Surgery on Children with Congenital Heart Disease Due to Trisomy 18 to Promote Transition to the Home Environment

1岐阜県総合医療センター小児循環器内科Department of Pediatric Cardiology, Gifu Prefectural General Medical Center ◇ Gifu, Japan

2岐阜県総合医療センター小児心臓外科Department of Pediatric Cardiac Surgery, Gifu Prefectural General Medical Center ◇ Gifu, Japan

受付日:2019年3月29日Received: March 29, 2019
受理日:2019年7月12日Accepted: July 12, 2019
発行日:2019年11月1日Published: November 1, 2019





Background: For children with congenital heart disease (CHD) resulting from trisomy 18, we do not perform intracardiac repair; instead, we opt for palliative surgery when their parents wish to proceed with surgical intervention.

Methods: From hospital medical records, we retrospectively identified 17 patients whose attending physicians had consulted our department between January 2010 and September 2016. We classified patients into two groups: those who required surgical intervention for CHD to promote transition to the home environment and who underwent surgery with parental consent (Group I: 5 patients), and those who did not require surgical intervention for CHD and did not undergo surgery (Group N: 12 patients). We compared the ease of transition to life in the patient’s own home between Group I and Group N.

Results: The median survival of the patients was 427 days in Group I and 173.5 days in Group N (p=0.0534). The median number of days spent in the patients’ own homes was 647 days in Group I and 72 days in Group N (p=0.0495).

Conclusion: Palliative surgery for CHD in patients with trisomy 18 extended the period of time that patients and their families could spend together in the home environment following hospital discharge.

Key words: trisomy 18; congenital heart disease; cardiac surgery; hospital discharge; prognosis

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