日本小児循環器学会雑誌 Pediatric Cardiology and Cardiac Surgery

Online ISSN: 2187-2988 Print ISSN: 0911-1794
特定非営利活動法人日本小児循環器学会 Japanese Society of Pediatric Cardiology and Cardiac Surgery
〒162-0801東京都新宿区山吹町358-5アカデミーセンター Japanese Society of Pediatric Cardiology and Cardiac Surgery Academy Center, 358-5 Yamabuki-cho, Shinju-ku, Tokyo 162-0801, Japan
Pediatric Cardiology and Cardiac Surgery 34(3): 155-159 (2018)
doi:10.9794/jspccs.34.155

症例報告Case Report

遺伝性不整脈合併母体の妊娠出産Pregnancy in Women with Inherited Primary Arrhythmia Syndromes

神戸市立医療センター中央市民病院小児科Department of Pediatrics, Kobe City Medical Center General Hospital ◇ Hyogo, Japan

受付日:2018年3月2日Received: March 2, 2018
受理日:2018年5月18日Accepted: May 18, 2018
発行日:2018年9月1日Published: September 1, 2018
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挙児希望のある致死性の遺伝性不整脈Inherited Primary Arrhythmia Syndromes (IPAS)合併女性に対し安全な妊娠分娩管理を行うことは重要であるが,その分娩管理方針は未だ確立していない.IPAS合併母体妊娠分娩管理方針の根拠となる臨床情報を収集,蓄積しすることを目的とし,当院周産期センターにおいて2008~2016年に入院したCPVT合併母体3例(疑い1例)6出産,LQT2合併母体1例1出産について診療録を後方視的に検討した.全例小児循環器科医,産科医,麻酔科医,循環器内科医,新生児科医の連携による集学的妊娠分娩管理を計画・実施し,1例を除きβ-blocker内服下に在胎37週から38週台での予定帝王切開を選択し,母児共に重大な心イベントなく管理可能であった.IPAS合併母体の妊娠出産についてはまだ症例数が少なく,疫学的情報および症例の集積は重要であると考える.

Providing safe management to enable women with inherited primary arrhythmia syndromes (IPAS) to have babies is very important, but no management policy has yet been established. To obtain clinical information about pregnancy in women with IPAS and provide an input on the development of a management policy, we retrospectively reviewed the clinical records of six pregnancies in three patients with catecholaminergic polymorphic ventricular tachycardia (one suspected case) and one pregnancy in one patient with long QT syndrome in our hospital from 2008 to 2016. We held multidisciplinary meetings with obstetricians, cardiologists, anesthesiologists, and neonatologists to develop a detailed plan. With the exception of one patient, we selected a planned cesarean section between 37 and 38 weeks of gestation; there were no cardiac events. In the pursuit of a secure management strategy, the accumulating of additional clinical information and cases of pregnancy in women with IPAS is needed.

Key words: Inherited Primary Arrhythmia Syndromes (IPAS); Catecholaminergic Polymorphic Ventricular Tachycardia (CPVT); Long QT Syndrome (LQTS); pregnancy

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This page was last modified on 2018-09-11T14:58:58.403+09:00


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